I-Antiphospholipid syndrome kusho ukuthi igazi lomuntu liqukethe ama-antibodies ngokumelene nezinhlobo ezithile ze-phospholipids. Uma ungazange uthathe inkambo yakamuva ekolishi yezoloji (futhi iningi lethu alikho), i-phospholipids iyinhlangano evamile futhi edingekile yamangqamuzana omuntu namaseli ezinengi ezinye izidalwa eziphilayo.
Sibutsetelo
Lapho umuntu enezifo ezilwa ne-phospholipids, lokhu kungabangela ama-clots amancane egazini lomuntu futhi kwandise ukuthambekela ekubhekeni kwegazi okubalulekile, njenge-vein thrombosis ejulile.
I-Antiphospholipid syndrome ikwandisa ingozi yezinkinga eziningi zempilo ezihlukene, kusukela ekuhlukunyezweni kuya ezinkingeni zenhliziyo.
I-Antiphospholipid syndrome ingabangelwa isifo esizimele, njenge-lupus noma kungaba yisimiso esiyisisekelo ngaphandle kwesifo esaziwayo sokuzimela.
Isigameko
Amaphesenti angaba ngu-2 ukuya kwangu-4 emiphakathini yabantu jikelele ine-antiphospholipid antibodies, futhi ngaphezu kwengxenye yalabo abane-antiphospholipid antibody syndrome eyinhloko. I-Antiphospholipid syndrome iyinhlangano engamaphesenti angaba ngu-15 wabesifazane abanokukhubazeka okuphindaphindiwe. Amaphesenti angaba ngu-10 abantu abatholwa ukuthi bane-antiphospholipid syndrome ekugcineni bayotholakala benesifo sokuzimela.
Ubudlelwane nemikhawulo ejwayelekile ejwayelekile
Abacwaningi bathole ukuthi ukuba ne-antiphospholipid syndrome kungakwandisa amathuba omama okwehlukaniswa okuphindaphindiwe. Isizathu salokhu akucacile; abanye abacwaningi bakholelwa ukuthi i-antiphospholipid syndrome ibangela ama-clots amancane egazi ukuze ivimbele ukunikezwa kwegazi ku-placenta.
Abanye bakholelwa ukuthi ukulwa ne-antiphospholipid syndrome kungase kuphazamise ikhono leqanda elikhushulelwe ukufaka emgqeni wesibeletho.
I-Antiphospholipid syndrome isungulwe kahle njengesizatfu sezinkinga zokukhubazeka esikhathini esizayo kepha odokotela basalokhu baqiniseki ngendima yokuthi ama-antibospholipid antibodies angase adlale ekukhulelweni kokuqala kokuqala.
Izimpawu
Iningi labantu abane-antiphospholipid antibodies ayinayo izimpawu, nakuba lesi sifo singabangela izingxenyana zegazi nezinye izinkinga zempilo kwabanye abantu. Kulabo besifazane, ukulahlekelwa kwesisu okuphindaphindiwe kungase kube yodwa uphawu lwesifo.
Ukuxilongwa
Ukuthola i-antiphospholipid syndrome kungaba yinselele; ukuhlolwa okujwayelekile kwamagciwane e- lupus anticoagulant kungathembeki futhi ukuzwela kungashintsha ngokusekelwe ejenti elisetshenziselwa i-laboratory ngayinye. Ngokuvamile, uma ucabangela i-antiphospholipid syndrome njengento engenzeka ekutheni imithwalo yezinsizwa eziphindaphindiwe, odokotela bafuna umuntu ukuba abe nesifo samaphilisi e-lupus anticoagulant noma ama-anticardiolipin antibodies ngaphezu kwesinye isikhathi ngaphambi kokuthola ukuxilongwa. Qaphela ukuthi ukuhlolwa okuhle kwamagciwane e-lupus anticoagulant akusho ukuthi umuntu une-lupus yesifo.
Ukwelashwa nokubikezelwa
Abesifazane abaye bathola ukuthi banesifo se-antiphospholipid syndrome cishe bangamaphesenti angama-70 amathuba okukhulelwa okuphumelelayo nokwelashwa, okuvame ukuqukethe i -aspirin ephansi ephansi kanye / noma imishanguzo ye-heparin . Nakuba lokhu ukwelashwa kuthuthukisa imiphumela yokukhulelwa yabesifazane abane-antiphospholipid syndrome, lezi zindlela zokwelapha zingandisa amazinga ezinkinga zokukhulelwa kwezintathu ezintathu, kodwa-ke, ngakho-ke abesifazane abano-antiphospholipid syndrome ngokuvamile badinga ukubona onguchwepheshe obungozi kakhulu futhi banakekelwa njalo ngaphambi kokukhulelwa.
Ngenxa yokuthi i-antiphospholipid syndrome ingahlotshaniswa nezinye izidakamizwa zezempilo, ama-OB / GYN avame ukululeka abesifazane abaye bahlola ukuthi isimo sinokuxhumana nomsebenzi jikelele noma isazi sokuqapha isimo ngemuva kokukhulelwa. Ezinye ze-OB / GYN zeluleka ngokusetshenziswa kokuvimbela ukukhulelwa kwe-hormonal kwabesifazane abanomlando we-antiphospholipid syndrome futhi, ngenxa yengozi engeziwe yezindwangu zegazi.
Imithombo:
I-Bertolaccini, i-ML ne-MA Khamashta, "I-Laboratory yokuxilongwa nokuphathwa kwezinselelo kule-antiphospholipid syndrome." Lupus 2006.
U-Empson, M., M. Lassere, J. Craig, noJack Scott, "Ukuvimbela ukukhulelwa kwesisu okuqhubekayo kwabesifazane abane-antiphospholipid antibody noma i-lupus anticoagulant. I- Cochrane Database ye-Systemic Reviews 2005.
I-Rai, i-RS "Antiphospholipid syndrome kanye nokukhulelwa kwesisu okuphindaphindiwe." I-Journal of Postgraduate Medicine 2002.
I-University of Illinois - i-Urbana / Champaign, i- "Antiphospholipid Syndrom." Imithombo yeziguli .