I-Amniotic band syndrome yinkinga eyenzeka cishe ngayinye ku-1,200 kuya kweyodwa kuzo zonke izinhlobo ezingu-15,000 zokuzalwa. Lokhu kwenza kube yinto engavamile ukuba nakho, nakuba kulinganiselwa ukuthi kwenzeka cishe ku-178 kuzo zonke izinhlobo zokukhubazeka kwezingu-10 000. Imiphumela yalesi simo ingaba isakazeke, ihlukahluka, futhi idlulele ebangeni kusukela komnene kuya kunzima.
Izimbangela
Ngenkathi kusengabikho izimpendulo ezicacile mayelana nokuthi yini ebangela i-amniotic band syndrome, inkolelo ehamba phambili yukuthi ukukhathazeka ekukhulelwe kwangaphambili kuholela kule nkinga.
Isikhwama se- amniotic sakhiwe izingqimba ezimbili, i-amnion, ne-chorion. I-amnion ingqimba elisondelene nengane yakho. Lezi zigaba ezimbili zincane kakhulu futhi zinamathelana komunye nomunye, kodwa zisasebenza ngokwahlukana.
Amniotic band syndrome kwenzeka lapho izingxenye ze-amnion, ungqimba lwangaphakathi lwe-sac amniotic, liphuka. Imigqa ye-sac amniotic ingakwazi ukunamathela noma iwele izingxenye zomntwana-lezi yizibopho. Ukunamathela kungavimbela ukukhula, ukugeleza kwegazi, noma kokubili. Lokhu kungabangela uchungechunge oluyinkimbinkimbi lweziphambeko zokuzalwa, ngokuvamile ezidijithali ezingekho noma izitho, ukugcoba, kanye nezinye izimo eziphuthumayo.
Kucatshangwa ukuthi ama-amniotic bands angenzeka ekukhulelweni kokuqala futhi ekukhulelweni kwesikhathi sekwephuzile kusuka ekungeneni okungahleliwe ekukhulelweni. Uma lezi ziphuka zenzeka ngesikhathi sokukhulelwa zinganquma ukuthi izimo ezinzima zizoba nzima kangakanani kumntwana. Isibonelo, kusenesikhathi, izingozi zibhubhisa kakhulu, kanti iqembu elibonakala kamuva ekukhulelwe lingenalo nhlobo.
I-Amniotic Band Syndrome Yenzani Ngomntwana Wami?
Kukhona uhlu oluyinkimbinkimbi lwezinkinga ezingenzeka ezihlobene nalesi simo. Ezinye zalezi zincane, kuyilapho ezinye ziyinkimbinkimbi kakhulu noma zingase zibulale. Nakhu eminye yemiphumela emihle evela kulokhu:
- Izinsimbi zokuqeda noma ukulahlekelwa izingxenye noma amadijithi aphelele (iminwe nezinzwane)
- Izindandatho zokulahlekelwa noma ukulahlekelwa izingxenye noma izitho zomzimba wonke (izingalo nemilenze)
- Ukuvuvukala okwedlulele komzimba okwedlule ibhande
- Izandla zeClub noma izinyawo zeqembu (ukuguquka okukhulu kwezandla noma izinyawo)
- I-Cleft lip kanye / noma i-palate (ihlukaniswe emlonyeni noma emlonyeni)
- Ukukhubazeka ebusweni
- Ukukhubazeka komgogodla
- I-Thoracosisis (i-constriction yodonga lwe-thoracic)
- Izidakamizwa zodonga zasisu
- I-Encephalocele (i-neural tube defect lapho ingxenye yobuchopho idlula khona nge-skull)
- I-Anencephaly (i-neural tube defect lapho ingxenye yebuchopho ne-skull ilahlekile)
- Ukuqothulwa komgudu womzimba (ukunikezwa kwegazi emthonjeni we-umbilical, ngakho-ke umntwana, kunqunywe)
- I-Limb-body-wall complex (inhlanganisela yenkinga ehilela izitho, futhi ngokuvamile isifuba noma isisu somntwana)
Izinkinga Ezinokwenzeka Ngokukhulelwa
Nakuba ukukhathazeka kwakho ngomntanakho kubaluleke kakhulu engqondweni yakho, kunezindaba ezinhle ngoba lokhu akuyona into evame ukushintsha ubude bakho bokukhulelwa. Iningi labesomama abanakho izingozi ezengeziwe ngokwabo noma ukukhulelwa kwabo. Nakuba kungase kube khona ingozi encane yokuletha ingane yakho ngaphambi kwesikhathi.
Inkinga eyodwa engase ingakhulumi ngokwanele kuyoba ukukhathazeka komphakathi nangokomzwelo wokuba nosana olunenkinga njengoba kunzima njengaleli.
Futhi, uma ubheka ukuthi akuzona eziningi ezinye izinsana ezinalezi zinkinga, ukuthola ukusekelwa kwabazali abaye besesimweni sakho kungenzeka kube lula njengoba ungathemba.
Kunezinsiza ezithile ze-intanethi kanye nezindaba ezivela kwezinye imindeni eziye zabhekana nalesi simo, abaningi abazimisele ukuhlanganyela nawe. Yize kungenzeka ukuthi kungenzeka ukuthi ngeke ukwazi ukuthola umuntu onemibandela efanayo, unikezwe ububanzi bamathuba. Uma ukwazi ukungena kwelinye lamaziko e-fetal enza ukwelashwa ukuphatha i-amniotic band syndrome, bangase babe nenethiwekhi yokusekela engcono ekwakheni.
Uma kungekho abanye abantu abaye bahlangabezana nezimo ezifanayo, ukukhuluma nabaqeqeshi ababhekana nabazali enkingeni kungasiza. I-perinatologist yangakini noma i-neonatal enkulu yokunakekela iyunithi ingase ibe nohlu lwemithombo, ngisho nangaphambi kokuba ingane yakho izalwe.
Izingozi Zezingozi
Njengazo zonke izixazululo ekukhulelwe, sivame ukubheka ukuthi kungani lokhu kwenzeka. Iqiniso liwukuthi sisazama ukuthola isizathu esiqondile se-amniotic band syndrome, esiyinkimbinkimbi ekubukeni kwezici zobungozi. Lokhu kuyinkimbinkimbi futhi ngoba kuyinto engavamile. Lokho kusho ukuthi sinokunye okuholela kulokho okungakwandisa ingozi yalesi sixazululo esingavamile.
Ucwaningo olulodwa lubheke inani elincane kakhulu labesifazane kodwa lithola ukuthi labo ababenokuhlinzwa kokubeletha kwabanomzimba babenezibalo eziphakeme ze-amniotic band syndrome. Esinye isifundo sibheke izingozi zale nkinga emva kwe-chorionic sampling sampling (CVS). Lokhu kuvivinywa kofuzo lwe-genetic, lapho ezinye ze-chorionic villi zisuswe ukuze zithole izimo zofuzo ezinganeni. I-hypothesis yukuthi i-puncturing ye-sac amniotic ukuze uthole lokho okubangela ukuthi i-banding ivele. Kukhona nombuzo wokuthi ngabe izingozi ezifanayo zingasebenza yini kumniocentesis , eyenziwa kamuva ekukhulelwe.
Kwakukhona olunye ucwaningo oluthile olwalukhombisa ukuthi kunokwanda kwe-amniotic band syndrome lapho umama evezwe yiMisoprostol yezidakamizwa ekukhulelwe kakhulu. Lokhu kuvame ukunikezwa njengendlela yokukhipha isisu, hhayi imithi ejwayelekile yokunikezwa kwabesifazane abakhulelwe.
Kunezici ezinobungozi ezingase zikwazi ukudala izinhlobo eziningi zokukhubazeka nezinkinga zokukhulelwa okufanele zinciphise noma zisuswe uma kungenzeka. Lokho kuhlanganisa:
- Ukubhema ekukhulelweni
- Ukusetshenziswa kwezidakamizwa ekukhulelwe
Ngingazi kanjani Uma Ingane Yami Imine Amniotic Band Syndrome?
I-Amniotic band syndrome ivame ukutholakala ku-ultrasound, kodwa ngokuvamile hhayi ngemva kweviki leshumi nambili lokukhulelwa. Kuyoba khona izindawo ezibonwe yi-ultrasound uchwepheshe ukuze ufunde kabanzi. Lokhu ngokuvamile kuvame ukuhlola okungeziwe noma ngaphezulu okujulile i-ultrasound noma kungenzeka i-MRI. I-MRI nayo iyoba usizo ekuhloleni ukuthi umonakalo omkhulu wenziwe kanjani. Ezinye izivivinyo ezingase zibekwe zihlanganisa:
- I-Ultrasound ehlosiwe (i-3D)
- Ucwaningo Lwegazi Lwegazi Lama-Doppler
- I-Fetal Echocardiogram
Ukuvimbela
Njengamanje, ayikho indlela eyaziwa ukuvimbela i-amniotic band syndrome ukuthi ingenzeki. Ngenkathi sibona ukuthi amanye amacala angase ahilele ukuhlolwa okungahambi kahle kokubeletha, njenge-chorionic sampling sampling (CVS), izinombolo zabesifazane abakhetha ukuhlolwa okungahleliwe ziye zehla ngokuphawulekayo njengoba kuhlolwa okuncane okungenasidingo kuyatholakala.
Kunezincomo ezijwayelekile zokukhulelwa okunempilo okungalandelwa ukuqinisekisa ukubheja kwakho okuhle ngokunciphisa ukukhubazeka kokuzalwa. Lokhu kuvame ukuyingxenye yokunakekelwa kwangaphambili .
Izinkinga Zizobe Zikhulu Kangakanani?
Ubukhulu bezinkinga ezivela ku-amniotic band syndrome kuxhomeke ezintweni ezihlukahlukene. Lokhu kufaka hlangana ukuthoma kokukhulelwa okwenziwe emaceleni kumzimba womzimba noma ukuphuma. Ngaphambili ekuqaleni kokukhulelwa lokhu kwenzeka, izinkinga ziba nzima kakhulu.
Ukwelapha
Kunezindlela ezimbili ezikhona zokwelapha i-amniotic band syndrome: ngaphambi kokubeletha nge-optical fetal futhi emva kokubeletha ngezokwelapha ezihlukahlukene kanye nemithi yokwelapha. Ezimweni eziningi, i-amniotic band syndrome ngokuvamile ayitholakali kuze kube sekupheleni kokuzalwa. Ngokujwayelekile, kuleli phuzu, kunokukhathalela kuphela izimpawu kanye nokwelashwa ukuphatha umonakalo okungenzeka usuvele uvele. Lokhu kungabandakanya ukwelashwa ngokomzimba, ukuhlinzwa kwamathambo, ukuhlinzwa ngomlomo kanye nokwenziwa kwe-maxillofacial, noma ngisho nokunakekelwa kwe-palliative. Izindlela zokwelapha kanye nokuhlinzwa okusetshenzisiwe kuzoxhomekeka kunoma yiziphi izingxenye zomzimba ezithintekayo kanye nobukhulu bomonakalo.
Kunezinye izindlela ezintsha zokwelashwa ezenziwa ezindaweni ezimbalwa ezweni lonke lase-United States ngokusebenzisa ukuhlinzwa kwe-fetal ukuphatha amanye amacala we-amniotic band syndrome ngesikhathi sokukhulelwa. Nakuba akuzona zonke izimo ezifanele ukuhlinzekwa, lokhu kuyinkinga oyodinga ukuba nayo ngezobuchwepheshe. Ukuhlinzwa kokubeletha ngokuvamile kudinga ukuba uhambe kwenye yalezi zikhungo zokwelashwa nokuhlinzwa. Lokhu kungenzeka noma akusho ukuthi kuzodingeka uhlale eduze nesikhungo uze ubelethe.
Ukuhlinzwa kokubeletha, ithuluzi lepensile elisepilini lesisindo lifakwa esibelethweni. Isetshenziselwa ukuhlukanisa i-band ukukhulula ibhande kude nomlenze noma ingxenye yomzimba. Ngezinye izikhathi imiphumela iyamangalisa, kanti omunye udokotela ohlinzayo uthi, ngokushesha uma usebenzisa i-laser ukususa ibhande kusukela emlenzeni womntwana, umlenze uphenduka uphinde uphinde uphindze uphinde ubuyekeze igazi.
Izimpikiswano Nezinhlekelele Zokuhlinzwa Kwe-Fetal
Ukusetshenziswa kokuhlinzwa kokubeletha ekunakekeleni i-amniotic band syndrome akuyona ingxabano. Izinhlobo ezimbili ezivame kakhulu zokuhlinza zihilela ukususa ibhendi elisongela umthamo we-umbilical, okuyinto, ngaphandle kokuhlinzwa, ingane ingase ife; noma ukususa ibhande ukuvimbela ukukhishwa kwesigungu.
Izingozi zokuhlinzwa zifaka ukutheleleka, izinkinga ezivela ku-anesthesia, ukulethwa ngaphambi kwesikhathi, nezinye izinkinga. Lezi zingozi zingase zibulale futhi zisho ukuthi akuwona wonke umuntu osekela ukwenza ukuhlinzwa kokubeletha ukuze asindise isilungu, ngoba, nakuba kunzima, ukukhishwa kwesigungu akuyona into ebulalayo. Lezi zinkinga zokuziphatha phakathi kwabazali, abahlinzeki, namakomiti okuziphatha ezibhedlela ezahlukeneyo.
Akuzange kube khona ukuhlinza noma izifundo eziningi, kodwa izifundo ezincane ezenziwe zikhombisa izinga eliphumelelayo lokuphumelela ngamaphesenti angama-50. Lokhu akuzwanga njengezinga elikhulu lokuphumelela, kodwa kunikezwe ukuhlolwa kokuhlinzwa kokubeletha kanye nezingozi ezengeziwe zokudinga ukuqhubeka nokukhulelwa, lokhu kubhekwa njengezinga eliphezulu lokuphumelela. Ithemba lokuthi ukuhlinzekwa okuqhubekayo okwenziwe, kuphakama lesi silinganiso sokuphumelela kuyoba. Lokhu kuncike ekutholeni amacala aphezulu, kodwa futhi ekuhlanzeni inqubo kanye nokulandelwa kwezinqubo.
Ingabe Lokhu Kuzokwenzeka Futhi?
Uma uzwa lokhu ngesikhathi ukhulelwe, ungase uzibuze ukuthi lokhu kuzokwenzeka yini esikhathini esizayo sokukhulelwa. Lokhu kubhekwa njenge-syndrome engeyona ephindaphindiwe, okusho ukuthi ngeke kwenzeke futhi. Nakuba kusobala ukuthi ungakwazi ukugwema izici ezingase zibe yingozi noma ukunciphisa noma ukunciphisa okwenzekayo, ungase ukwazi ukuzitholela ukuthula kwengqondo.
Amanye Amagama
Kunamagama amaningi okuthi i-amniotic band syndrome ingabizwa. Lokhu kufaka:
- Isifo se-Amniotic sequence
- I-Amniotic banding
- I-Constriction ring syndrome
- Ama-Streeter bands
- ADAM ukulandelana
> Imithombo:
> Amniotic Band Syndrome. Ukukhathazeka Kwesisusa Isikhungo Sezingane Zase-Wisconsin. http://www.chw.org/medical-care/fetal-concerns-center/conditions/infant-complications/amniotic-band-syndrome/
> Amniotic Band Syndrome. Inhlangano Kazwelonke Yezifo Ezinzima (NORD). https://rarediseases.org/rare-diseases/amniotic-band-syndrome/
> Barzilay E, Harel Y, Haas J, Berkenstadt M, Katorza E, Achiron R, Gilboa Y. Ukuxilongwa kwangaphambi kokubeletha kwe-amniotic band syndrome - izinto eziyingozi kanye nezibonakaliso ze-ultrasonic. I-Matern Fetal Fetal Neonatal Med. 2015 Feb; 28 (3): 281-3. doi: 10.3109 / 14767058.2014.915935. Epub 2014 Meyi 22.
> Cignini, P., Giorlandino, C., Padula, F., Dugo, N., Cafà, EV, & Spata, A. (2012). I-Epidemiology kanye nezici zobungozi be-amniotic band syndrome, noma ukulandelana kwe-ADAM. Umagazini weMithi Yokubeletha , 6 (4), 59-63.
> Javadian P, Shamshirsaz AA, Haeri S, Ruano R, Ramin SM, Cass D, Olutoye OO, Belfort MA. Umphumela we-Perinatal ngemuva kokukhishwa kwama-amniotic ama-fetoscopic ama-band: okuhlangenwe nakho okukodwa kanye nokubuyekezwa kwezincwadi. I-Gynecol ye-Ultrasound Obstet. 2013 Oct; 42 (4): 449-55. i-doi: 10.1002 / uog.12510.